Cervico-thoracic kyphosis in a girl with Pierre Robin sequence
نویسندگان
چکیده
Congenital cervico-thoracic kyphosis has been encountered in a girl with Pierre Robin sequence. The constellation of the spine malformation complex such as incomplete development of the vertebral bodies associated with defective ossification of the cervico-thoracic pedicles causing effectively the development of complete spinal cord injury at the kyphotic level of C7/T1 were present. Congenital kyphosis secondary to vertebral body hypoplasia has not been reported in connection with Pierre Robin sequence.
منابع مشابه
Role of SOX9 in the Etiology of Pierre-Robin Syndrome
Objective(s:Cleft lip/palate are common congenital anomalies, affecting approximately 2/1000 live births. Pierre Robin Sequence is a subgroup of the cleft palate population. Chromosomal abnormalities near the SOX9 gene disrupt the regulation of this gene and prevent the SOX9 protein from properly controlling the development of facial structures, which leads to isolated PRS. The present study wa...
متن کاملاانجام بیهوشی عمومی برای خدمات دندانپزشکی یک بیمار مبتلا به Pierre Robin Sequence: گزارش مورد
مقدمه:Pierre Robin Sequence که قبلاً به عنوان سندروم پیر روبین نامیده میشد، شامل سه ناهنجاری مادرزادی ماندیبول کوچک، عقب افتادگی زبان و شکاف کام میباشد. به طوری که نقص اولیه عامل ایجاد نقص بعدی است. نوزادان مبتلا به این بیماری با مشکلات انسداد راه هوایی، بازگشت محتویات معده به مری وتغذیه همراهند. مداخلات صورت گرفته اغلب جهت حفظ یک راه هوایی باز است. شرح مورد: یکی از مشکلات اصلی با توجه به کو...
متن کاملOne lung ventilation for children with Pierre Robin sequence using SupremeTM LMA and Arndt endobronchial blocker: a case report
One lung ventilation (OLV) is a technique routinely used in thoracic anesthesia to facilitate thoracic surgery. We describe a case of pediatric with Pierre Robin sequence using SupremeTM laryngeal mask airway (LMA) and Arndt endobronchial blocker to achieve OLV.
متن کاملThe Effect of Spine Strengthening Exercises and Posture Training on Functional Thoracic Hyper Kyphosis in Young Individuals
Background & Objective: Hyper- kyphosis negatively affects health status, physical mobility, and quality of life. Corrective exercise interventions are often utilized to manage subjects with thoracic hyper-hypnosis. The purpose of this study was to investigate the effectiveness of multimodal spine strengthening exercises (spinal strengthening, spinal alignment and other such exercises for incr...
متن کامل